Other Tests to Suspect or Exclude Forms of PH
- Medical History – rapid progression of symptoms (1 month), pre-syncope (signs of RV forward failure), new fluid retention (signs of RV backward failure)
- VQ Scan – no segmental V/Q mismatches (CTEPH excluded)
- CT Scan – Mild emphysema otherwise normal parenchyma
- PFT – FVC 2.9L (76%); FEV1 2L (66%); FEV1/FVC 69%; DLCO 61%
- Overnight Oximetry – no significant oxygen desaturation
- Lab – HIV nonreactive, ANA / RF negative
- 6MWD – 350 m, desats to 84% but recovers quickly at rest
Emily’s symptoms are progressing rapidly, and her echo is consistent with suspicion for high risk of PH.
Her 6MWD is significantly impaired. Her PFTs and V/Q scan excluded WHO Group 3 and 4 PH, respectively.